DOI: https://doi.org/10.15574/10.15574/PP.2017.72.125

Качество жизни детей, больных гемофилией а, связанное со здоровьем: мировой опыт и отечественные реалии

A. I. Markin, L. Ya. Dubey, Kh. M. Komendant, N. V. Dubey

Аннотация


Ведущее место в структуре наследственных нарушений гемостаза у детей занимает гемофилия А. Учитывая хроническое течение, потребность в регулярном пожизненном заместительном лечении, частые осложнения и инвалидизацию пациентов, из года в год растет интерес ученых и практических врачей к субъективной составляющей этого заболевания, а именно оценке качества жизни, связанной за здоровьем. Это нашло свое отражение в имплементации методик оценки качества жизни детей, больных гемофилией А, в теоретическую и практическую медицину. В данной статье сделана попытка анализа данных о качестве жизни, связанном со здоровьем детей, больных гемофилией А, и практических подходов к его оценке в мировой медицине и в Украине в частности.

Ключевые слова


гемофилия; качество жизни; дети

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Литература


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